Bullous Pemphigoid

WHAT IS IT?

Bullous pemphigoid refers to an autoimmune disorder that involves the skin. 

WHAT CAUSES IT?

Autoantibodies (IgG) against the hemidesmosome and basement membrane zone. 

WHY IS IT CONCERNING MEDICALLY?

This condition can cause very itchy bullae to form on the skin (which can be a nuisance to patients). 

WHAT IS THE INTIAL PRESENTATION?

Patient Chief Complaints:

  • Rash
  • Severe itching 

Detected Medical Problems:

  • Observed bullae on skin 
WHAT ARE IMPORTANT ELEMENTS OF THE MEDICAL HISTORY?

Risk Factors:

Medical History:

 

WHAT ARE IMPORTANT FEATURES OF THE PHYSICAL EXAM?

Vital Signs:

 

Other:

 

CLINICAL WORKUP: MICROSCOPY

Light microscopy (of a skin biopsy) reveals the presence of:

  • Sub epidermal cleavage

Immunofloresence (of a skin biopsy) reveals the presence of:

  • Linear IgG/C3 staining at the basement membrane (dermal/epidermal junction)
CLINICAL WORKUP: OTHER

 

HOW DO WE NARROW THE DIFFERENTIAL?

Conditions that present similarly and how to exclude them:

 

WHAT IS OUR THRESHOLD FOR DIAGNOSING THIS CONDITION?

 

 
PATIENT MANAGEMENT: DISEASE TREATMENT

Topical high-potency glucocorticoids are often the first-line treatment:

  • Clobetosol
PATIENT MANAGEMENT: PROPHYLACTIC MEASURES

 

COULD THIS HAVE BEEN PREVENTED?

 

ARCHIVE OF STANDARDIZED EXAM QUESTIONS 

This archive compiles standardized exam questions that relate to this topic.

 

Page Updated: 02.15.2017