Prader-Willi Syndrome

WHAT IS IT?

Prader-Willi syndrome is a genetic disorder.

WHAT CAUSES IT?

It is caused by a defect in the long arm of chromosome 15.

WHY IS IT A PROBLEM?

 

WHAT MAKES US SUSPECT IT?

Risk factors

 

Initial Presentation

  • Intellectual disability

History Of Present Illness

During infancy patient will often be underweight and have hypotonia

During childhood patient will have an increased appetite and obesity.

Physical Exam Findings

 

CLINICAL WORKUP

 

AT WHAT POINT DO WE CONFIDENT IN MAKING THE DIAGNOSIS?

 

WHAT ELSE ARE WE WORRIED ABOUT?

 

HOW DO WE TREAT IT? 

 

HOW WELL DO THE PATIENTS DO?

 

WAS THERE A WAY TO PREVENT IT?

 

OTHER FACTS?

 

ARCHIVE OF STANDARDIZED EXAM QUESTIONS 

This archive compiles standardized exam questions that relate to this topic.

 

FURTHER READING

DynaMed

UpToDate

 

Page Updated: 09.03.2016